2-oxoadipic acid

2-keto adipic acid a-keto adipic acid a-oxo adipic acid alpha-keto adipic acid adipic acid, 2-oxo- 2-oxo- hexane dioic acid 2-oxo hexanedioic acid 2-oxo- hexanedioic acid hexanedioic acid, 2-oxo- hexanedioic acid, 2-oxo- (7CI,8CI,9CI) 2-oxo hexanedionic acid PubMed: High-performance liquid chromatographic method for profiling 2-oxo acids in urine and its application in evaluating vitamin status in rats. PubMed: Production of superoxide/hydrogen peroxide by the mitochondrial 2-oxoadipate dehydrogenase complex. PubMed: Genetic basis of alpha-aminoadipic and alpha-ketoadipic aciduria. PubMed: Structure and function of a decarboxylating Agrobacterium tumefaciens keto-deoxy-d-galactarate dehydratase. PubMed: Time-dependent effects of L-tryptophan administration on urinary excretion of L-tryptophan metabolites. PubMed: Pantothenic acid deficiency may increase the urinary excretion of 2-oxo acids and nicotinamide catabolites in rats. PubMed: A dual conformation of the post-decarboxylation intermediate is associated with distinct enzyme states in mycobacterial KGD (α-ketoglutarate decarboxylase). PubMed: Fate of dietary tryptophan in young Japanese women. PubMed: DHTKD1 mutations cause 2-aminoadipic and 2-oxoadipic aciduria. PubMed: Homoisocitrate dehydrogenase from Candida albicans: properties, inhibition, and targeting by an antifungal pro-drug. PubMed: Enzyme redesign guided by cancer-derived IDH1 mutations. PubMed: Toward biotechnological production of adipic acid and precursors from biorenewables. PubMed: A network perspective on metabolic inconsistency. PubMed: Biomarkers in the early period of acute myocardial infarction in rat serum and protective effects of Shexiang Baoxin Pill using a metabolomic method. PubMed: Substrate specificity of 2-hydroxyglutaryl-CoA dehydratase from Clostridium symbiosum: toward a bio-based production of adipic acid. PubMed: Fluorometric determination of 2-oxoadipic acid, a common metabolite of tryptophan and lysine, by high-performance liquid chromatography with pre-chemical derivatization. PubMed: Unravelling the gallic acid degradation pathway in bacteria: the gal cluster from Pseudomonas putida. PubMed: Excess dietary lysine increases growth of chicks fed niacin-deficient diets, but dietary quinolinic acid has no niacin-sparing activity. PubMed: Quantitative acylcarnitine profiling in peripheral blood mononuclear cells using in vitro loading with palmitic and 2-oxoadipic acids: biochemical confirmation of fatty acid oxidation and organic acid disorders. PubMed: A Korean girl with alpha-aminoadipic and alpha-ketoadipic aciduria accompanied with elevation of 2-hydroxyglutarate and glutarate. PubMed: Gas chromatographic-mass spectrometric screening for organic acidemias using dried urine filter paper: determination of alpha-ketoacids. PubMed: Identification of the human mitochondrial oxodicarboxylate carrier. Bacterial expression, reconstitution, functional characterization, tissue distribution, and chromosomal location. PubMed: Identification in Saccharomyces cerevisiae of two isoforms of a novel mitochondrial transporter for 2-oxoadipate and 2-oxoglutarate. PubMed: Kearns-Sayre syndrome presenting as 2-oxoadipic aciduria. PubMed: Normal kynurenine metabolism in 2-oxoadipic aciduria. PubMed: Aspartate kinase-independent lysine synthesis in an extremely thermophilic bacterium, Thermus thermophilus: lysine is synthesized via alpha-aminoadipic acid not via diaminopimelic acid. PubMed: Alpha-keto acid chain elongation reactions involved in the biosynthesis of coenzyme B (7-mercaptoheptanoyl threonine phosphate) in methanogenic Archaea. PubMed: Identification of strictly conserved histidine and arginine residues as part of the active site in Petunia hybrida flavanone 3beta-hydroxylase. PubMed: Abnormal alpha-aminoadipic acid excretion in a newborn with a defect in platelet aggregation and antenatal cerebral haemorrhage. PubMed: Determination of glutamine and alpha-ketoglutarate concentration and specific activity in plasma using high-performance liquid chromatography. PubMed: Inactivation of alpha-ketoglutarate dehydrogenase during oxidative decarboxylation of alpha-ketoadipic acid. PubMed: Alpha-keto acids are novel siderophores in the genera Proteus, Providencia, and Morganella and are produced by amino acid deaminases. PubMed: Identification of N-acetyl-alpha-aminoadipic acid in the urine of a patient with alpha-aminoadipic and alpha-ketoadipic aciduria. PubMed: A fatal case of 2-keto-, 2-hydroxy- and 2-aminoadipic aciduria: relation of organic aciduria to phenotype? PubMed: The sub-cellular localisation and regulatory properties of pyruvate carboxylase from Rhizopus arrhizus. PubMed: alpha-Aminoadipic and alpha-ketoadipic aciduria: detection of a new case by a screening program using two-dimensional thin layer chromatography of amino acids. PubMed: Capillary gas chromatographic/mass spectrometric analysis of abnormal metabolites in hypoglycin-treated rat urine. PubMed: A patient with alpha-ketoadipic and alpha-aminoadipic aciduria. PubMed: Tryptophan and lysine metabolism in alpha-aminoadipic aciduria. PubMed: Biochemical and clinical studies of a new case of alpha-aminoadipic aciduria. PubMed: Metabolism of alpha-aminoadipic and alpha-ketoadipic acids: studies using rat and beef liver, and human leukocytes. PubMed: Alpha-ketoadipic aciduria: a description of a new metabolic error in lysine-tryptophan degradation. PubMed: Alpha-ketoadipic aciduria, a new inborn error of lysine metabolism; biochemical studies. PubMed: Enzymatic formation of alpha-ketoadipic acid from homoisocitric acid. PubMed: BIOSYNTHESIS OF ALPHA-KETOADIPIC ACID BY EXTRACTS OF BAKER'S YEAST. PubMed: Enzymatic conversion of homoisocitric acid into alpha-ketoadipic acid. PubMed: Biosynthesis of Lysine from alpha-Ketoadipic Acid and alpha-Aminoadipic Acid in Yeast.