cerotic acid

hexacosanoic acid hexacosanoicacid 1- hexyldecanoate PubMed: High hexacosanoic acid levels are associated with coronary artery disease. PubMed: High hexacosanoic acid levels are associated with coronary artery disease. PubMed: Reductions in neuronal peroxisomes in multiple sclerosis grey matter. PubMed: New flavan and alkyl alpha,beta-lactones from the stem bark of Horsfieldia superba. PubMed: An electrospray ionisation-mass spectrometry screening of triacylglycerols in developing cultivated and wild peanut kernels (Arachis hypogaea L.). PubMed: Zellweger syndrome - a lethal peroxisome biogenesis disorder. PubMed: Chemical composition of the fatty oils of the seeds of Cleome viscosa accessions. PubMed: Arabidopsis ECERIFERUM9 involvement in cuticle formation and maintenance of plant water status. PubMed: The effect of bone marrow transplantation on oxidative stress in X-linked adrenoleukodystrophy. PubMed: The inflammatory response in acyl-CoA oxidase 1 deficiency (pseudoneonatal adrenoleukodystrophy). PubMed: Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation. PubMed: Inhibition of saturated very-long-chain fatty acid biosynthesis by mefluidide and perfluidone, selective inhibitors of 3-ketoacyl-CoA synthases. PubMed: A mixture of oleic, erucic and conjugated linoleic acids modulates cerebrospinal fluid inflammatory markers and improve somatosensorial evoked potential in X-linked adrenoleukodystrophy female carriers. PubMed: Is subclinical adrenal failure in adrenoleukodystrophy/adrenomyeloneuropathy reversible? PubMed: Active components from Siberian ginseng (Eleutherococcus senticosus) for protection of amyloid β(25-35)-induced neuritic atrophy in cultured rat cortical neurons. PubMed: Screening assay of very long chain fatty acids in human plasma with multiwalled carbon nanotube-based surface-assisted laser desorption/ionization mass spectrometry. PubMed: [Chemical constituents of rhizomes of Zingiber officinale]. PubMed: Phytochemical investigation of the fruit peels of Citrus reticulata Blanco. PubMed: Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy. PubMed: Lovastatin in X-linked adrenoleukodystrophy. PubMed: Investigation of stratum corneum lipid model membranes with free fatty acid composition by neutron diffraction. PubMed: Very long chain fatty acid levels in patients diagnosed with multiple sclerosis. PubMed: Fast diffusion of very long chain saturated fatty acids across a bilayer membrane and their rapid extraction by cyclodextrins: implications for adrenoleukodystrophy. PubMed: A fast method for the identification of Mycobacterium tuberculosis in sputum and cultures based on thermally assisted hydrolysis and methylation followed by gas chromatography-mass spectrometry. PubMed: [Studies on chemical constituents of aerial roots of Ficus microcarpa]. PubMed: Odd-numbered very-long-chain fatty acids from the microbial, animal and plant kingdoms. PubMed: X-linked adrenoleukodystrophy: clinical course and minimal incidence in South Brazil. PubMed: Epicuticular lipids induce aggregation in Chagas disease vectors. PubMed: Concentrations of very long-chain fatty acid in whole blood are associated with cardiovascular risk factors in children. PubMed: Plasmalogens participate in very-long-chain fatty acid-induced pathology. PubMed: A key role for the peroxisomal ABCD2 transporter in fatty acid homeostasis. PubMed: Early oxidative damage underlying neurodegeneration in X-adrenoleukodystrophy. PubMed: A simple and sensitive liquid chromatographic method for the analysis of free docosanoic, tetracosanoic and hexacosanoic acids in human plasma as fluorescent derivatives. PubMed: High levels of saturated very long-chain fatty acid (hexacosanoic acid; C26:0) in whole blood are associated with metabolic syndrome in Japanese men. PubMed: Fatty acid interdigitation in stratum corneum model membranes: a neutron diffraction study. PubMed: RNAi-mediated silencing of ABCD3 gene expression in rat C6 glial cells: a model system to study PMP70 function. PubMed: [Studies on chemical constituents of Heterosmilax yunnanensis]. PubMed: Hexacosanoic and docosanoic acids plasma levels in patients with cerebral childhood and asymptomatic X-linked adrenoleukodystrophy: Lorenzo's oil effect. PubMed: New flavonoids and other constituents from Lespedeza cuneata. PubMed: Down-regulation of fatty acid synthase increases the resistance of Saccharomyces cerevisiae cells to H2O2. PubMed: Induction of lipid peroxidation and decrease of antioxidant defenses in symptomatic and asymptomatic patients with X-linked adrenoleukodystrophy. PubMed: Characterization of glycoinositolphosphoryl ceramide structure mutant strains of Cryptococcus neoformans. PubMed: Novel free ceramides as components of the soldier defense gland of the Formosan subterranean termite (Coptotermes formosanus). PubMed: Compounds with DNA cleaving activity from Kadsura ananosma. PubMed: Combined liquid chromatography-tandem mass spectrometry as an analytical method for high throughput screening for X-linked adrenoleukodystrophy and other peroxisomal disorders: preliminary findings. PubMed: The effect of Lorenzo's oil on oxidative stress in X-linked adrenoleukodystrophy. PubMed: Follow-up of 89 asymptomatic patients with adrenoleukodystrophy treated with Lorenzo's oil. PubMed: A novel coaxial electrospray ionization method for characterizing hexacosanoylceramides by Fourier transform ion cyclotron resonance mass spectrometry. PubMed: [Studies on the constituents from the stems of Spatholobus suberectus]. PubMed: Very long chain fatty acids activate NADPH oxidase in human dermal fibroblasts. PubMed: Constituents of Carapa guianensis Aubl. (Meliaceae). PubMed: [Studies on the chemical constituents of Chinese herb Melastoma dodecandrum]. PubMed: An HPLC-MS approach for analysis of very long chain fatty acids and other apolar compounds on octadecyl-silica phase using partly miscible solvents. PubMed: Evidence that oxidative stress is increased in patients with X-linked adrenoleukodystrophy. PubMed: Free radical release in C6 glial cells enriched in hexacosanoic acid: implication for X-linked adrenoleukodystrophy pathogenesis. PubMed: Antimicrobial activity of terpenoids from Trichodesma amplexicaule Roth. PubMed: [Lipid compounds from Echinacea purpurea]. PubMed: [Studies on the chemical constituents of Zanthoxylum dimorphophyllum Hemsl. var spinifolium Rhed. et Wils]. PubMed: [Studies on the chemical constituent of Ephedra likiangensis]. PubMed: [Clinical heterogeneity of X-linked adrenoleukodystrophy ]. PubMed: Diagnostic patterns of very-long-chain fatty acids in plasma of patients with X-linked adrenoleukodystrophy. PubMed: Correlations of elevated levels of hexacosanoate in erythrocyte membranes with risk factors for atherosclerosis. PubMed: Testosterone metabolites in patients reduce the levels of very long chain fatty acids accumulated in X-adrenoleukodystrophic fibroblasts. PubMed: Lovastatin therapy for X-linked adrenoleukodystrophy: clinical and biochemical observations on 12 patients. PubMed: Inactivation of the inhA-encoded fatty acid synthase II (FASII) enoyl-acyl carrier protein reductase induces accumulation of the FASI end products and cell lysis of Mycobacterium smegmatis. PubMed: Role of a new mammalian gene family in the biosynthesis of very long chain fatty acids and sphingolipids. PubMed: Progression of abnormalities in adrenomyeloneuropathy and neurologically asymptomatic X-linked adrenoleukodystrophy despite treatment with "Lorenzo's oil". PubMed: Very long-chain fatty acids in Rett syndrome. PubMed: Determination of very-long-chain fatty acids in serum by gas chromatography-nitrogen-phosphorus detection following cyanomethylation. PubMed: Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls. PubMed: A new HPLC-based method for the quantitative analysis of inner stratum corneum lipids with special reference to the free fatty acid fraction. PubMed: Inhibition of a Mycobacterium tuberculosis beta-ketoacyl ACP synthase by isoniazid. PubMed: Abnormality of very long-chain fatty acids of erythrocyte membrane in alcoholic patients. PubMed: Use of gas chromatographic fatty acid and mycolic acid cleavage product determination to differentiate among Mycobacterium genavense, Mycobacterium fortuitum, Mycobacterium simiae, and Mycobacterium tuberculosis. PubMed: Increased very long-chain fatty acids in erythrocyte membranes of patients with aceruloplasminemia. PubMed: A new peroxisomal beta-oxidation disorder in twin neonates: defective oxidation of both cerotic and pristanic acids. PubMed: Effects of exogenous hexacosanoic acid on biochemical myelin composition in weaning and post-weaning rats. PubMed: Very long-chain fatty acid pattern in crush syndrome patients in the Kobe earthquake. PubMed: Plasma phospholipid fatty acids in X-linked adrenoleukodystrophy. PubMed: Interactions of a very long chain fatty acid with model membranes and serum albumin. Implications for the pathogenesis of adrenoleukodystrophy. PubMed: Mycobacterium branderi sp. nov., a new potential human pathogen. PubMed: Measurement of peroxisomal fatty acid beta-oxidation in cultured human skin fibroblasts. PubMed: Dietary management of X-linked adrenoleukodystrophy. PubMed: Beta-oxidation of fatty acids in cultured human skin fibroblasts devoid of the capacity for oxidative phosphorylation. PubMed: Profiles of very-long-chain fatty acids in plasma, fibroblasts, and blood cells in Zellweger syndrome, X-linked adrenoleukodystrophy, and rhizomelic chondrodysplasia punctata. PubMed: Studies on the effect of fenoprofen on the activation and oxidation of long chain and very long chain fatty acids in hepatocytes and subcellular fractions from rat liver. PubMed: Mycobacterium celatum sp. nov. PubMed: Isolation and characterization of eceriferum (cer) mutants induced by T-DNA insertions in Arabidopsis thaliana. PubMed: Altered adrenocortical response under the influence of experimentally increased serum very long chain fatty acids in rats. PubMed: Fatty acid synthesis from [2-14C]acetate in normal and peroxisome-deficient (Zellweger) fibroblasts. PubMed: Diagnosis of peroxisomal disorders with neurological involvement. PubMed: Characterization of a distinct group of slowly growing mycobacteria by biochemical tests and lipid analyses. PubMed: Schizophrenic patients treated with high dose phenothiazine or thioxanthene become deficient in polyunsaturated fatty acids in their thrombocytes. PubMed: Phospholipids in X-linked adrenoleukodystrophy white matter: fatty acid abnormalities before the onset of demyelination. PubMed: Neonatal seizures and severe hypotonia in a male infant suffering from a defect in peroxisomal beta-oxidation. PubMed: Oxidation of very-long-chain fatty acids in rat brain: cerotic acid is beta-oxidized exclusively in rat brain peroxisomes. PubMed: Conclusive evidence that very-long-chain fatty acids are oxidized exclusively in peroxisomes in human skin fibroblasts. PubMed: Long-chain-acyl-CoA synthetase and very-long-chain-acyl-CoA synthetase activities in peroxisomes and microsomes from rat liver. An enzymological study. PubMed: [Chemical constituents of the pericarp of Trichosanthes rosthornii Harms]. PubMed: Determination of very-long-chain fatty acids in plasma by a simplified gas chromatographic-mass spectrometric procedure. PubMed: Central nervous system malformations and white matter changes in pseudo-neonatal adrenoleukodystrophy. PubMed: Infantile phytanic acid storage disease, a disorder of peroxisome biogenesis: a case report. PubMed: Adrenomyeloneuropathy presenting as Addison's disease in childhood. PubMed: Dietary erucic acid therapy for X-linked adrenoleukodystrophy. PubMed: Gas chromatography of mycobacterial fatty acids and alcohols: diagnostic applications. PubMed: Capillary gas chromatographic analysis of mycolic acid cleavage products, cellular fatty acids, and alcohols of Mycobacterium xenopi. PubMed: Phytanic acid, pristanic acid, and very-long-chain fatty acid methyl esters measured simultaneously by capillary gas chromatography. PubMed: Very long-chain fatty acids in erythrocyte membrane phospholipids in adrenoleukodystrophy. PubMed: Hexacosanoate contents in Japanese common foods. PubMed: [Two adult cases of adrenoleukodystrophy with clinical features of striatonigral degeneration--a probable variant of adrenoleukodystrophy]. PubMed: Impaired ability of peroxisomes to activate very-long-chain fatty acids in X-linked adrenoleukodystrophy. PubMed: Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids. PubMed: Carrier detection for adrenoleukodystrophy by high-performance liquid chromatography. PubMed: Influence of structural modifications on the phase behavior of semi-synthetic cerebroside sulfate. PubMed: Treatment of infantile phytanic acid storage disease: clinical, biochemical and ultrastructural findings in two children treated for 2 years. PubMed: Effects of long-chain, saturated fatty acids on membrane microviscosity and adrenocorticotropin responsiveness of human adrenocortical cells in vitro. PubMed: Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders. PubMed: Very long chain fatty acid beta-oxidation by rat liver mitochondria and peroxisomes. PubMed: Prenatal diagnosis of Zellweger syndrome by measurement of very long chain fatty acid (C26:0) beta-oxidation in cultured chorionic villous fibroblasts: implications for early diagnosis of other peroxisomal disorders. PubMed: Electronmicroscopic study on biopsied rectal mucosa in adrenoleukodystrophy. PubMed: Beta-oxidation of very-long-chain fatty acids and their coenzyme A derivatives by human skin fibroblasts. PubMed: Adrenoleukodystrophy: from bedside to molecular biology. PubMed: Adrenoleukodystrophy: dietary oleic acid lowers hexacosanoate levels. PubMed: A new dietary therapy for adrenoleukodystrophy: biochemical and preliminary clinical results in 36 patients. PubMed: Adrenoleukodystrophy: biochemical procedures in diagnosis, prevention and treatment. PubMed: A simple method to diagnose adrenoleukodystrophy using a dried blood spot on filter paper. PubMed: Adrenoleukodystrophy. Report of an autopsy case with adrenoleukomyeloneuropathy. PubMed: Very long-chain fatty acids in erythrocyte membrane sphingomyelin: detection of ALD hemizygotes and heterozygotes. PubMed: Analysis of mycolic acid cleavage products and cellular fatty acids of Mycobacterium species by capillary gas chromatography. PubMed: Adrenoleukodystrophy: oleic acid lowers fibroblast saturated C22-26 fatty acids. PubMed: Metabolism of [17,18-3H2]hexacosanoic acid and [15,16-3H2]lignoceric acid in cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN). PubMed: Very long-chain fatty acids in neutral lipids and glycerophospholipids of adrenoleukodystrophy-cultured skin fibroblasts. PubMed: [EMG and evoked potentials in adrenomyeloneuropathy]. PubMed: Adrenoleukodystrophy without adrenal insufficiency and its magnetic resonance imaging. PubMed: Disturbed very long chain (C24-C26) fatty acid pattern in fibroblasts of patients with Zellweger's syndrome. PubMed: First trimester prenatal diagnosis of adrenoleukodystrophy by determination of very long chain fatty acid levels and by linkage analysis to a DNA probe. PubMed: [Adult disclosure of a case of familial adrenoleukodystrophy]. PubMed: Determination of C20-C30 fatty acids by reversed-phase chromatographic techniques: an efficient method to quantitate minor fatty acids in serum of patients with adrenoleukodystrophy. PubMed: Plasma and skin fibroblast C26 fatty acids in infantile Refsum's disease. PubMed: The design of a diet restricted in saturated very long-chain fatty acids: therapeutic application in adrenoleukodystrophy. PubMed: Biochemical evidence for clinically diagnosed adrenoleucodystrophy in two brothers. PubMed: The cerebrohepatorenal (Zellweger) syndrome. Increased levels and impaired degradation of very-long-chain fatty acids and their use in prenatal diagnosis. PubMed: Serum very long chain fatty acid pattern in Zellweger syndrome. PubMed: The prenatal diagnosis of adrenoleukodystrophy. Demonstration of increased hexacosanoic acid levels in cultured amniocytes and fetal adrenal gland. PubMed: Increased synthesis of hexacosanoic acid (C23:0) by cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN). PubMed: Abnormality of long-chain fatty acids in erythrocyte membrane sphingomyelin from patients with adrenoleukodystrophy. PubMed: Specificities of human and rat brain enzymes of cholesterol ester metabolism toward very long chain fatty acids: implication for biochemical pathogenesis of adrenoleukodystrophy. PubMed: Fatty acid patterns in brain, fibroblast, leukocyte and body fluid lipids in adrenoleukodystrophy. PubMed: Adrenoleukodystrophy: evidence that abnormal very long chain fatty acids of brain cholesterol esters are of exogenous origin. PubMed: Adrenoleukodystrophy: elevated C26 fatty acid in cultured skin fibroblasts. PubMed: Constituents of Nealchornea yapurenis (Euophorbiaceae). PubMed: Metabolic studies of adrenoleukodystrophy.