glutaconic acid

trans- glutaconate (E)- glutaconic acid pent-2-ene-1,5-dioic acid (2E)- pent-2-enedioic acid (E)- pent-2-enedioic acid 2- pentene dioic acid (2E)-2- pentenedioic acid 2- pentenedioic acid, (2E)- PubMed: One-pot formation of 2,4-di- or 2,4,6-tri-olefinic monocarboxylic acids by straight chain C4-extension. PubMed: Experimental Evidence of Long-Range Intramolecular Vibrational Energy Redistribution through Eight Covalent Bonds: NIR Irradiation Induced Conformational Transformation of E-Glutaconic Acid. PubMed: Favourable Outcome in Two Pregnancies in a Patient with 3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency. PubMed: Metabolic changes in rat serum after administration of suberoylanilide hydroxamic acid and discriminated by SVM. PubMed: Proposed recommendations for diagnosing and managing individuals with glutaric aciduria type I: second revision. PubMed: An Integrated Multi-Omic Approach to Assess Radiation Injury on the Host-Microbiome Axis. PubMed: Clinical and molecular investigation in Chinese patients with glutaric aciduria type I. PubMed: Base-catalyzed bicyclization of dialkyl glutaconates with cinnamoylacetamides: a synthetic strategy for isoquinolinedione derivatives. PubMed: Diagnosis by whole exome sequencing of atypical infantile onset Alexander disease masquerading as a mitochondrial disorder. PubMed: Catalytic asymmetric Tamura cycloadditions. PubMed: Brain MRI findings as an important diagnostic clue in glutaric aciduria type 1. PubMed: Neurotoxic effects of trans-glutaconic acid in rats. PubMed: Diagnosis and management of glutaric aciduria type I--revised recommendations. PubMed: Production of glutaconic acid in a recombinant Escherichia coli strain. PubMed: Effects of structural analogues of the substrate and allosteric regulator of the human mitochondrial NAD(P)+-dependent malic enzyme. PubMed: Efficient synthesis and neuroprotective effect of substituted 1,3-diphenyl-2-propen-1-ones. PubMed: Guideline for the diagnosis and management of glutaryl-CoA dehydrogenase deficiency (glutaric aciduria type I). PubMed: Basidiochrome -- a novel siderophore of the Orchidaceous Mycorrhizal Fungi Ceratobasidium and Rhizoctonia spp. PubMed: Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency. PubMed: Vascular dysfunction as an additional pathomechanism in glutaric aciduria type I. PubMed: 99mTc-labeling and in vitro and in vivo evaluation of HYNIC- and (Nalpha-His)acetic acid-modified [D-Glu1]-minigastrin. PubMed: 3-Hydroxyglutaric acid fails to affect the viability of primary neuronal rat cells. PubMed: [Glutaric aciduria type 1: an example of the importance of early detection of so-called cerebral organic aciduria]. PubMed: On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1. PubMed: Plausible molecular mechanism for activation by fumarate and electron transfer of the dopamine beta-mono-oxygenase reaction. PubMed: Hydrogen-bonded complexes of 2-pyridone with centrosymmetric and non-centrosymmetric dicarboxylic acids. PubMed: Induction of the mitochondrial permeability transition in vitro by short-chain carboxylic acids. PubMed: Sensitivity and specificity of free and total glutaric acid and 3-hydroxyglutaric acid measurements by stable-isotope dilution assays for the diagnosis of glutaric aciduria type I. PubMed: 3-Methyl glutaconic aciduria in Iraqi Jewish children may be misdiagnosed as cerebral palsy. PubMed: Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I. PubMed: Subdural hemorrhage as an initial sign of glutaric aciduria type 1: a diagnostic pitfall. PubMed: Sodium ion-dependent hydrogen production in Acidaminococcus fermentans. PubMed: Chronic subdural hematoma, as an initial manifestation of glutaric aciduria type-1. PubMed: Organic acid and acylcarnitine profiles of glutaric aciduria type I. PubMed: A biotin-dependent sodium pump: glutaconyl-CoA decarboxylase from Acidaminococcus fermentans. PubMed: 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in an infant with macrocephaly and mild metabolic acidosis. PubMed: The identification of (E)-2-methylglutaconic acid, a new isoleucine metabolite, in the urine of patients with beta-ketothiolase deficiency, propionic acidaemia and methylmalonic acidaemia. PubMed: Glutaconate CoA-transferase from Acidaminococcus fermentans. PubMed: The reversible dehydration of (R)-2-hydroxyglutarate to (E)-glutaconate. PubMed: Glutaric aciduria: clinical and laboratory findings in two brothers. PubMed: Glutaconic acid, a product of the fermentation of glutamic acid by Peptococcus aerogenes.